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 Definitions of farber lipogranulomatosis  

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Definition of 'farber lipogranulomatosis' U.S. National Library of Medicine 

1.  farber lipogranulomatosis
A sphingolipidosis subtype that is characterized by the histological appearance of granulomatous deposits in tissues. It results from the accumulation of CERAMIDES in various tissues due to an inherited deficiency of ACID CERAMIDASE.



'farber lipogranulomatosis' - Nearby Entries  

fanconi anemia complementation group proteins  fanconi syndrome  fanft  farber lipogranulomatosis  farnesol  farnesyl-diphosphate farnesyltransferase  farnesyltranstransferase  



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